Dec 10, 2018 henoch schonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. Henoch schonlein purpura hsp, was first recognized in 1801 by heberden and first described as an association arthritis by schonlein in 1837. Background 1st described in 1801 by william heberden, a physician in london, who wrote about a case of a 5 year old boy with hematuria, abdominal pain, joint pains and skin rash. Henoch schonlein purpura hsp in spanish espanol download print friendly pdf. Information on henoch schonlein purpura hsp in children. The treatment of henoch schonlein purpura is directed toward the most significant area of involvement.
Henochschonlein purpura hsp is the most common vasculitis in children, characterized by triad of symptoms. The prognosis for patients with henoch schonlein purpura is generally excellent. Please use one of the following formats to cite this article in your essay, paper or report. Henochschonlein purpura is a disease that causes small blood vessels in the body to become inffamed and leak. Hsp presents with purple spots on the skin purpura, arthralgia, digestive problems, and kidney injury. Diagnostic and management of henoch schonlein purpura. Risk of long term renal impairment and duration of follow up recommended for henochschonlein purpura with normal or minimal urinary findings. Henochschonlein purpura hsp is a vasculitis inflam mation of the blood vessels, usually involving the immune system. Henochschonlein purpura hsp is an autoimmune disorder that is due to the production of autoantibodies against some of the bodys. Schonleinhenoch purpura is the most common infantile vasculitis and is mostly clinically diagnosed. Schonleinhenoch purpura, anaphylactoid purpura rhumatoid purpura diagnosis diagnosis of hsp is established when at least 2 of the following 4 criteria are present. Alicia isabel pascual perez, begona dominguez aurrecoechea, alejandra mendez sanchez, vanessa moya dionisio, helena aparicio casares, lucia rodriguez garcia, flor angel ordonez alvarez. Palpable purpura age henoch schonlein purpura hsp is an immunemediated vasculitis. The most striking feature of this form of vasculitis is a purplish rash, typically on the lower legs and buttocks.
Henoch schonlein purpura causes skin rash, pain in the abdomen, and joint inflammation. The source of information was medical records and a data gathering guide containing the studied variables was used. Late onset was the only variable related to recurrence p jul 24, 2019 henoch schonlein purpura also known as iga vasculitis is a disorder that causes the small blood vessels in your skin, joints, intestines, and kidneys to become inflamed and bleed. Background 1st described in 1801 by william heberden, a physician in london, who wrote about a. The small vessels of the skin, joints, kidneys, and digestive organs are particularly involved. Henochschonlein purpura nord national organization for.
Purpura not due to a low platelet count, caused by inflammation in blood vessels of the skin, is the hallmark of hsp. Henoch schonlein purpura hsp is an immunoglobulina. Abdominal symptoms occur in 70% of cases, with possible intussusception or intestinal perforation. Their clinical manifestations included palpable purpura in 100%, subcutaneous edema in 30%, arthritisarthralgia in 78%, gastrointestinal.
Henochschonlein purpura hsp is an immunemediated vasculitis. There is some evidence to support steroid therapy in the treatment of severe abdominal pain, severe nephritis, and central nervous system involvement. It is the most common form of childhood vascular inflammation vasculitis and results in inflammatory changes in the small blood vessels. Henoch schonlein purpura is a vasculitis usually with a benign course. Henoch schonlein purpura guidelines henoch schonlein purpura hsp is the commonest vasculitis of childhood which is selflimiting in majority of cases. Henochschonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. Iga vasculitis, formerly henochschonlein purpura, is a form of vasculitisa family of rare disorders characterized by inflammation of the blood vessels, which can restrict blood flow and damage vital organs and tissues. Iga immunoglobulin a vasculitis causes inflammation and bleeding of the small blood vessels of the skin, joints.
This article is part of an expert video encyclopedia. Henochschonlein purpura hsp is a rare inflammatory disease of the small blood vessels capillaries and is usually a selflimited disease. Frequently, hsp leads to abdominal pain and intestinal bleeding, renal involvement and joint pain. Henochschoenlein purpura is a leukocytoclastic vasculitis of childhood characterized by abdominal pain, bloody diarrhea, petechiae, and potential risk of renal involvement. Endoscopy of the small bowel shows ulcerous hemorrhagic enteritis, together with a wide range of elementary lesions. Evolucion torpida en nina con antecedentes familiares llamativos. Henochschonlein purpura hsp is the most common childhood vasculitis with an incidence of approximately 10 per 100 000 children. Precedidas por una infecciondel tracto respiratorio superiorpatologia mediada por elsistema inmuneinducida por factoresambientales. A retrospective descriptive study of patients with scholeinhenoch purpura diagnosis was conducted for. Schonlein henoch purpura is the most common infantile vasculitis and is mostly clinically diagnosed. Therapy for children with henochschonlein purpura nephritis. Their clinical manifestations included palpable purpura in 100%, subcutaneous edema in 30%, arthritisarthralgia in 78%, gastrointestinal involvement in 56% and renal abnormalities in 30%. Henochschonlein purpura hsp is a form of blood vessel inflammation or vasculitis. Although the disease has been described for over a century.
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